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[Congenital dermatofibrosarcoma protuberans: a case report]
C Muniesa1, N Curcó, X Pagerols
1Servicio de Dermatología. Hospital Mútua de Terrassa. Barcelona. España. cristinamuniesa@hotmail.com
Actas Dermo-Sifiliograficas
|October 27, 2007
Summary
Dermatofibrosarcoma protuberans is a rare skin cancer. This report details a rare congenital case in a 10-year-old boy, highlighting successful surgical management without recurrence.
Area of Science:
- Oncology
- Dermatology
- Pediatric Oncology
Background:
- Dermatofibrosarcoma protuberans (DFSP) is a rare, low-grade fibrohistiocytic skin tumor.
- Typically affecting adults aged 20-50, DFSP presents as a plaque or macule, progressing to nodular lesions.
- Congenital DFSP is exceptionally rare, with only 27 cases documented globally.