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Published on: June 16, 2023
Variability in the preoperative management of infants with hypoplastic left heart syndrome
B A Johnson1, K Mussatto, M R Uhing
1Department of Pediatrics, Division of Cardiology, Children's Hospital of Wisconsin, Medical College of Wisconsin, Milwaukee, WI 53226, USA. bethajohnson@hotmail.com
Insights
Preoperative care for infants with hypoplastic left heart syndrome (HLHS) lacks consistency. Further research is needed to determine optimal management strategies for these complex pediatric patients before surgery.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Neonatal Surgery
Background:
- Infants with hypoplastic left heart syndrome (HLHS) require early surgical intervention.
- Optimal preoperative management strategies for HLHS infants are not well-defined.
- Current preoperative care is often anecdotal and varies significantly.
Purpose of the Study:
- To describe current preoperative management practices for infants with HLHS.
- To identify variability in care among healthcare institutions.
- To highlight the need for evidence-based guidelines.
Main Methods:
- A survey was designed to assess preoperative management.
- The questionnaire covered management styles, monitoring techniques, and institutional characteristics.
- Responses from healthcare providers were compiled and analyzed.
Main Results:
- A significant lack of consistency in preoperative management techniques for HLHS infants was observed.
- Variability exists in ventilatory management, enteral feeding, and monitoring.
- The impact of these diverse preoperative strategies remains unknown.
Conclusions:
- Current preoperative care for infants with HLHS demonstrates considerable inconsistency.
- Prospective randomized trials are necessary to evaluate different management strategies.
- Such trials should focus on ventilatory support, nutrition, and monitoring to improve outcomes.
Abstract:
Infants with hypoplastic left heart syndrome (HLHS) commonly undergo initial surgical palliation during the first week of life. Few data exist on optimal preoperative management strategies; therefore, the management of these infants prior to surgery is anecdotal and variable. To more fully define this variability in preoperative care of infants with HLHS, a survey was designed to describe current preoperative management practices in the infant with HLHS. The questionnaire explored management styles as well as preoperative monitoring techniques and characteristics of the respondent's health care institution. The responses were compiled and are reported. A striking lack of consistency in preoperative management techniques for infants with HLHS is apparent. The impact of these preoperative strategies is unknown. Despite challenges in anatomic and hemodynamic variability at presentation, a prospective randomized controlled trial comparing ventilatory management techniques, enteral feeding strategies, and the utility of various monitoring tools on short- and long-term outcome is needed.
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