Persistent left SVC with absent right SVC: a rare anomaly

Area of Science:

• Cardiology
• Congenital Heart Disease
• Vascular Anatomy

Background:

• Persistent left superior vena cava (PLSVC) is a known congenital anomaly.
• It is often associated with various congenital heart disorders.
• Absence of the right SVC is exceptionally rare, especially when occurring with PLSVC.

Observation:

• The case report details a patient with congenital absence of the right SVC.
• The patient also presented with a persistent left SVC.
• An ostium secundum atrial septal defect was observed concurrently.

Findings:

• The study highlights an extremely rare case of isolated absence of the right SVC coupled with a persistent left SVC.
• This anatomical variation was found in conjunction with an ostium secundum atrial septal defect.
• The co-occurrence of these anomalies is clinically significant.

Implications:

• This rare vascular anomaly necessitates careful consideration during interventional cardiology procedures.
• Accurate diagnosis is crucial for planning and executing safe cardiac surgery.
• Understanding this anomaly aids in managing patients with complex congenital heart disease.