Bronchopulmonary foregut malformation in an adult

A 50-year-old man with repeated episodes of right epigastric pain was seen in our hospital. Chest computed tomography and angiography revealed several arteries feeding an enhanced large mass located in the right lower lobe region. A right lower lobectomy was done with a provisional diagnosis of an intralobar sequestration. A 5-mm duct that was lined with esophageal mucous membrane that tracked from the lower esophagus toward the sequestrated lung was detected. A bronchopulmonary foregut malformation (BPFM) was diagnosed based on the histological finding that the duct was composed of ciliated epithelium and smooth muscle layers. BPFM is a subgroup of pulmonary sequestrations that communicate with the gastrointestinal tract. In contrast to pulmonary sequestrations, 75% of BPFMs are located on the right side. Thus, a BPFM should be considered in patients with right-sided pulmonary sequestrations, and their gastrointestinal tracts should be examined.