Related Experiment Video
Updated: Jul 9, 2026
Laparoscopic Anatomical Liver Segment VII Resection with Liver Parenchymal Transection Following a Priority Approach
Published on: May 23, 2025
[Liver hernia. Prognosis and report of 11 cases]
E Sabbah-Briffaut1, V Houfflin-Debarge, R Sfeir
1Service de pathologie maternelle et foetale, clinique d'obstétrique, hôpital Jeanne-de-Flandre, CHRU de Lille, 1, rue Eugène-Avinée, 59037 Lille, France.
Insights
Exclusive hepatoceles, a liver-predominant hernia, present significant neonatal morbidity. This condition requires complex multidisciplinary care, impacting infant health outcomes.
Area of Science:
- Neonatal surgery
- Pediatric surgery
- Congenital anomalies
Context:
- Exclusive hepatocele is a rare congenital anomaly.
- Defined as a hernia predominantly containing the liver.
- Often associated with other fetal anomalies.
Purpose:
- To evaluate neonatal morbidity and mortality in exclusive hepatoceles.
- To assess outcomes in a series of 11 cases.
- To highlight the distinct nature of this condition.
Summary:
- Diagnosis occurred at a mean gestational age of 14.5 weeks.
- One case had abnormal karyotype (trisomy 13), leading to termination.
- Delivery at 38 weeks, mostly via Cesarean section.
- Significant morbidity included respiratory distress and digestive complications.
- One neonatal death occurred due to pulmonary hypoplasia.
Impact:
- Exclusive hepatoceles represent a distinct entity among omphaloceles.
- Morbidity is substantial, necessitating specialized multidisciplinary care.
- Outcomes highlight the complexity of managing these neonates.
Objectives:
Exclusive hepatocele is defined as a hernia containing in majority the liver with possibly some intestinal loops. This study was undertaken to evaluate neonatal morbidity and mortality in this series of exclusive hepatoceles.
Materials And Methods:
We reviewed 11 cases of exclusive hepatoceles with delivery at the hospital Jeanne-de-Flandre in the CHRU of Lille, in France.
Results:
The mean gestational age of diagnosis was 14.5+/-3.4 weeks of gestation. Karyotype determination was performed in 100% of cases: it was abnormal in one case of 11. One termination of pregnancy was performed because of trisomy 13. The mean gestational age at delivery was 38+/-1.8 weeks of gestation. Cesarean deliveries were performed in nine cases. Morbidity was important with: one case of fetal growth retardation on total hepatocele, three cases of severe respiratory distress, two cases of severe digestive complications. The mean length of stay was 42.8 days. The mean length of parenteral feeding was 14.4 days. Postnatal mortality concerned one child, which died because of a severe respiratory distress due to pulmonary hypoplasia.
Conclusion:
In this series, morbidity is thus important, making of exclusive hepatoceles a full entity among the omphaloceles. The multidisciplinary take care is more complex but conceivable.
