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Cardiomyopathy in children in Ahmedabad

V K Gandhi1, S B Dalal, J R Sharma

  • 1Department of Pediatrics, K.M. School of Post-graduates, V.S. General Hospital, Ahmedabad.

Indian Journal of Pediatrics
|September 1, 1991
PubMed

Insights

Pediatric cardiomyopathies, including dilated (DCM), restrictive (RCM), and hypertrophic (HCM), are most common in children aged 2-5 and 10-16 years. Despite treatment, advanced cases show a poor prognosis.

Area of Science:

  • Pediatric Cardiology
  • Cardiovascular Research
  • Clinical Pediatrics

Background:

  • Cardiomyopathies are a significant cause of heart disease in children.
  • Understanding the epidemiology and clinical presentation of pediatric cardiomyopathies is crucial for timely diagnosis and management.
  • Dilated cardiomyopathy (DCM), restrictive cardiomyopathy (RCM), and hypertrophic cardiomyopathy (HCM) are key types affecting the pediatric population.

Purpose of the Study:

  • To present a clinical study and follow-up of 20 children with various cardiomyopathies up to age 16.
  • To describe the common types of cardiomyopathy in the pediatric age group.
  • To outline the clinical presentation and prognosis of pediatric cardiomyopathies.

Main Methods:

  • A clinical study involving 20 children diagnosed with cardiomyopathy.
  • Follow-up of patients up to 16 years of age.
  • Analysis of clinical presentations and treatment responses.

Main Results:

  • Dilated cardiomyopathy (DCM) was the most common type, followed by restrictive cardiomyopathy (RCM) and hypertrophic cardiomyopathy (HCM).
  • Short-chain hydroxyacyl-CoA dehydrogenase deficiency (SHMD) presenting with cardiomyopathy was frequent in infancy and early childhood.
  • Cardiomyopathies most frequently presented between ages 2-5 and 10-16 years, with DCM showing near-equal distribution across these groups.

Conclusions:

  • Cardiomyopathies in children exhibit distinct age distributions for different types.
  • Clinical presentation varies among cardiomyopathy subtypes.
  • Despite aggressive treatment, advanced pediatric cardiomyopathies often have a rapidly downhill course and a poor general prognosis.

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