The temporal bone in the Johanson-Blizzard syndrome. A CT study
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J Braun1, A Lerner, R Gershoni-Baruch
1Department of Diagnostic Radiology, Rambam Medical Center, Haifa, Israel.
Pediatric Radiology
|January 1, 1991
Abstract:
The findings of thin-section high-resolution CT of the temporal bone in two children with Johanson-Blizzard syndrome are reported. In both cases an anomaly of the inner ear was found, consisting of bilateral cystic dilatation of the cochlea and the vestibulum. The possible etiologic basis for the hearing loss in this syndrome is discussed and the literature is reviewed.