Cystic choroid plexus papilloma with multiple mural nodules in an infant

Parisa Emami-Naeini1, Farideh Nejat, Mostafa El Khashab

  • 1Department of Neurosurgery, Children's Hospital Medical Center, Medical Sciences/University of Tehran, Tehran, Iran.

Insights

A pediatric case highlights a cystic choroid plexus papilloma presenting as increased head circumference and seizures. Complete surgical removal of enhancing nodules is crucial for a cure.

Area of Science:

  • Pediatric Neurology
  • Neuro-oncology
  • Surgical Pathology

Background:

  • A 13-month-old male infant presented with progressive macrocephaly, neurodevelopmental delay, and seizures.
  • History of increased intracranial pressure due to an arachnoid cyst managed with shunting, but symptoms persisted.

Observation:

  • Magnetic resonance imaging revealed an intraventricular cystic tumor.
  • The tumor exhibited intensely enhancing mural nodules.

Findings:

  • Surgical excision of the cyst and nodules was performed.
  • Histopathological analysis confirmed the diagnosis of cystic choroid plexus papilloma.

Implications:

  • Emphasizes the need for accurate evaluation of intracranial cystic lesions to avoid misdiagnosis.
  • Recommends total resection of enhancing nodules in cystic choroid plexus papilloma for complete tumor cure.
Abstract

Related Concept Videos