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Implantation of Total Artificial Heart in Congenital Heart Disease
Published on: July 18, 2014
Criss cross heart in a congenitally corrected transposition of the great arteries
Insights
Criss cross heart, a rare congenital heart anomaly, involves abnormal heart rotation. This case highlights a unique presentation in a 22-year-old woman with corrected transposition of great arteries.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Morphology
Background:
- Criss cross heart is an extremely rare congenital heart anomaly, comprising less than 0.1% of all such conditions.
- It is defined by an abnormal rotation of the heart along its longitudinal axis.
- Often associated with other cardiac defects like pulmonary stenosis, ventricular septal defects, or hypoplastic right ventricles, typically presenting neonatally.
Observation:
- This report details a rare case of criss cross heart.
- The patient is a 22-year-old woman.
- She was diagnosed with congenitally corrected transposition of great arteries.
Findings:
- The patient presented with a complex congenital heart anomaly.
- The diagnosis of criss cross heart was confirmed.
- Congenitally corrected transposition of great arteries was also identified.
Implications:
- This case expands the known clinical spectrum of criss cross heart.
- It underscores the possibility of late presentation in adulthood for certain congenital heart diseases.
- Further research into the embryology and long-term outcomes of criss cross heart is warranted.
Abstract:
Criss cross heart is an extremely rare anomaly accounting for less than 0.1% of congenital heart disease. It is characterized by an abnormal rotation of the heart on its long axis. Almost always there are associated cardiac anomalies such as pulmonary stenosis, ventricular septal defect, ventriculoarterial connection discord or hypoplasia of the tricuspid valve or right ventricle and thereby presenting in the neonatal period. We present a case of a 22 year old woman with a congenitally corrected transposition of great arteries and a criss cross heart.

