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Updated: Jul 7, 2026

Three-Dimensional Echocardiographic Method for the Visualization and Assessment of Specific Parameters of the Pulmonary Veins
Published on: October 28, 2020
[Congenital unilateral pulmonary vein atresia: imaging findings]
I Artero Muñoz1, F Serrano Puche, M I Padín Marín
1Departamento de Radiodiagnóstico. Hospital Regional Universitario Carlos Haya. Málaga. España. ivanartero@hotmail.com
Insights
Congenital unilateral pulmonary vein atresia, a rare condition, can present in adults. CT and MRI scans are valuable for diagnosing this rare vascular anomaly, especially in patients with symptoms like hemoptysis.
Area of Science:
- Cardiology
- Radiology
- Pediatric Medicine
Background:
- Congenital unilateral pulmonary vein atresia is an exceptionally rare condition.
- It typically manifests in childhood or adolescence with recurrent pulmonary infections or hemoptysis.
- Adult presentation of this anomaly is highly unusual.
Observation:
- This report details two cases of congenital unilateral pulmonary vein atresia.
- A 26-year-old woman presented with recurrent hemoptysis.
- A 3-year-old boy experienced bronchospasm and recurrent pneumonia since infancy.
Findings:
- While traditionally diagnosed via cardiac catheterization and pulmonary angiography, CT and MRI findings can aid diagnosis.
- Computed Tomography (CT) and Magnetic Resonance Imaging (MRI) are effective in diagnosing congenital unilateral pulmonary vein atresia.
- MRI is particularly adept at characterizing the specific vascular abnormalities involved.
Implications:
- Advanced imaging techniques like CT and MRI can facilitate earlier diagnosis of this rare condition.
- These imaging modalities offer a less invasive diagnostic approach compared to traditional methods.
- Recognizing imaging findings is crucial for timely management of congenital unilateral pulmonary vein atresia.
Abstract:
Congenital unilateral pulmonary vein atresia is a very rare anomaly that generally presents during childhood or adolescence as recurrent episodes of pulmonary infections or hemoptysis. Its presentation in adults is highly exceptional. We describe two patients with congenital unilateral pulmonary vein atresia: the first is a 26-year-old woman with recurrent episodes of hemoptysis, and the second is a three-year-old boy with a history of bronchospasm and recurrent pneumonia from the age of three months. Although the diagnosis has classically been reached using cardiac catheterization and pulmonary angiography, we think that the CT and MRI findings can enable the diagnosis of congenital unilateral pulmonary vein atresia in cases with compatible clinical presentation. We emphasize the capacity of MRI for characterizing the vascular anomaly present in these patients.
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