[Fibrodysplasia ossificans progressiva: orthopedic pitfalls and controversies]
R Rachkidi1, I Ghanem, F Dagher
1Service de chirurgie orthopédique, hôpital Hôtel-Dieu de France, université Saint-Joseph, boulevard Alfred-Naccache, Beyrouth, Liban. ramirachkidi@hotmail.com
Abstract:
Fibrodysplasia ossificans progressiva (FOP) is a rare disorder of the connective tissue associating malformation of the great toes and progressive heterotopic ossifications. Diagnosis is mostly clinical and currently no treatment is available. We report on the case of an 8 year old boy having an unusual form of FOP. We discuss clinical aspects of the disease and insist on the importance of early diagnosis, avoiding harmful events and therapeutic pitfalls.
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