Primary Ewing's sarcoma of the petroclival bone

A 17-year-old male presented with signs of raised intracranial tension and multiple cranial nerve dysfunction. Radiological imaging revealed an extradural calcified tumor involving the right petrous bone and adjacent clivus. The patient underwent extensive surgical debulking of the mass. Histopathological study revealed that the tumor was Ewing's sarcoma. Post-operative radio- and chemotherapy were administered. The patient's cranial nerve dysfunctions had recovered to some extend at 12 months' follow-up. Ewing's sarcoma arising from the skull base is an extremely rare lesion. The relevant literature on the subject is reviewed.