[Congenital retinal macrovessels: a discovery by chance]

Congenital retinal macrovessels, where an aberrant retinal vessel, usually a venule, is present in the posterior pole and may cross the avascular foveal region, are seen rarely.

Most of these cases are unilateral and stable with excellent visual prognosis and are detected on routine examination. Foveal cysts, hemorrhages and displaced foveola may also be seen. These entities must be distinguished from racemose angiomas, capillary hemangiomas of the retina and even when associated with neurological symptoms, should be considered as part of the Wyburn-Masson syndrome.