Fontan operation and the single ventricle

Jamil A AboulHosn1, David M Shavelle, Yelba Castellon

  • 1Ahmanson-UCLA Adult Congenital Heart Disease Center, Los Angeles, CA, USA. JAboulhosn@mednet.ucla.edu

Insights

The Fontan operation has evolved significantly since 1971. This case study reviews 40 years of interventions for single ventricle patients, highlighting the Fontan procedure and cardiac CT angiography for complex circulation evaluation.

Area of Science:

  • Cardiology
  • Pediatric Cardiac Surgery
  • Medical Imaging

Background:

  • The Fontan operation, first described in 1971, is a palliative surgical procedure for complex single-ventricle congenital heart defects.
  • Over four decades, the Fontan operation has undergone numerous modifications and improvements to enhance patient outcomes.

Observation:

  • This study details the comprehensive medical, surgical, and percutaneous interventions for a single ventricle patient over 40 years.
  • The evolution of the Fontan procedure, including its indications, sequelae, and complications, is traced through this patient's case.

Findings:

  • Cardiac computed tomography with angiography (CCTA) is presented as a valuable noninvasive tool for assessing the intricate Fontan circulation.
  • The case illustrates the long-term management challenges and the importance of advanced imaging in Fontan patients.

Implications:

  • Understanding the historical development and long-term sequelae of the Fontan operation is crucial for managing complex congenital heart disease.
  • Noninvasive imaging modalities like CCTA play a vital role in the surveillance and management of patients with Fontan physiology.

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