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Updated: Jul 6, 2026
Robotic Cochlear Implantation for Direct Cochlear Access
Published on: June 16, 2022
Cochlear implantation results in patients with Kearns-Sayre syndrome
Sipke Pijl1, Brian D Westerberg
1School of Audiology and Speech Sciences, University of British Columbia, Vancouver, BC, Canada. SPijl@providencehealth.bc.ca
Objectives:
To examine the evidence for a cochlear, retrocochlear, or central site of lesion for deafness in two cochlear implant recipients with Kearns-Sayre Syndrome (KSS).
Design:
Speech perception data and electrically evoked Auditory Brainstem (eABR) and Middle Latency Responses were obtained in two patients with KSS and compared with a group of non-KSS implant recipients.
Results:
Speech perception data and electrophysiological responses for the patients with KSS were similar to those obtained in non-KSS patients.
Conclusions:
Results are consistent with an initial cochlear site of lesion for deafness in KSS, and with relative sparing of the central auditory pathway early in the disease.