Clinical features of syndromic craniosynostosis
1Departments of Orthodontics and Craniofacial Development, King's College London, London, UK; Department of Orthodontics, University of Helsinki, Helsinki, Finland.
Abstract:
Disruption of normal suture development and function can result in premature suture fusion, craniosynostosis. This review focuses on syndromic forms of craniosynostosis. More than 100 syndromes in which craniosynostosis is a feature have been documented and here the most common conditions including Apert and Crouzon syndromes are described as well as other conditions with a particularly interesting molecular etiology, such as Saethre- Chotzen and craniofrontonasal syndrome.
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