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Updated: Jul 6, 2026

Robotic Myotomy and Partial Fundoplication for Achalasia
Published on: August 11, 2023
Esophageal achalasia of unknown etiology in infants
Vijay D Upadhyaya1, A N Gangopadhyaya, D K Gupta
1Department of Pediatric Surgery, IMS, BHU, Varanasi, India. upadhyayavj@rediffmail.com
Insights
Achalasia cardia is rare in infants, often presenting with respiratory issues or vomiting mistaken for GER. Surgical intervention, esophagocardiomyotomy, provided significant symptom relief and weight gain in most cases.
Area of Science:
- Pediatric Surgery
- Gastroenterology
Background:
- Achalasia cardia is an uncommon pediatric condition, particularly in infants.
- Respiratory symptoms and vomiting (of uncurdled milk) are common in infantile achalasia and can be misdiagnosed as gastroesophageal reflux (GER).
Purpose of the Study:
- To present a series of pediatric achalasia cases.
- To highlight the diagnostic challenges and treatment outcomes in infantile achalasia.
Main Methods:
- Retrospective analysis of 8 pediatric achalasia cases over 12 years.
- Diagnosis confirmed by clinical examination and barium studies.
- Surgical treatment involved esophagocardiomyotomy with an antireflux procedure via abdominal route.
Main Results:
- Seven out of eight patients survived the surgical procedure.
- Post-operative follow-up showed remarkable symptom relief and satisfactory weight gain.
- One case of achalasia associated with alacrimia was noted; one infant was initially misdiagnosed with gastric volvulus.
Conclusions:
- Esophageal achalasia is a rare pediatric disease with often indeterminate origin.
- Achalasia cardia should be considered in the differential diagnosis of infants presenting with esophageal obstruction symptoms.
Background:
Achalasia cardia is an uncommon disease in children particularly in infants. We present 8 cases of achalasia who were encountered over a 12-year period. In infantile achalasia, respiratory symptoms predominate and vomiting may easily be mistaken for gastroesophageal reflux (GER). Vomiting of uncurdled milk is characteristic of achalasia.
Methods:
In this retrospective study, the data were obtained from records of the Department of Pediatric Surgery IMS, BHU Varanasi, India. The patients were diagnosed by clinical examination and barium study. Any other associated anomalies were noted in these patients. The patients underwent esophagocardiomyotomy with antireflux procedure via the abdominal route.
Results:
In the present series, 7 patients survived. The follow-up study after operation showed remarkable relief of symptoms with satisfactory weight gain. No post-operative death occurred in the patients. Achalasia associated with alacrimia was noted in one infant who was lost to follow up. One infant was initially diagnosed as having gastric volvulus, but exploration revealed achalasia cardia.
Conclusions:
Esophageal achalasia is a rare disease in children and its origin is generally indeterminable. Achalasia cardia should be emphasized in the differential diagnosis of an infant presenting with signs and symptoms of esophageal obstruction.
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