Related Experiment Video
Updated: Jul 5, 2026

Standardized Technique of Aortic Valve Re-implantation for Valve-sparing Aortic Root Replacement
Published on: December 11, 2017
Aortic valve replacement in a patient with morquio syndrome
Francesco Nicolini1, Domenico Corradi, Silvia Bosio
1Department of Cardiac Surgery, University of Parma, Parma, Italy. francesco.nicolini@unipr.it
Abstract:
Cardiac involvement in Morquio syndrome, mucopolysaccharidosis IV, is characterized by aortic and mitral valve thickening and infiltration of the coronary arteries. There are few reports concerning surgical interventions in patients with mucopolysaccharidoses. We report a case of a patient affected by Morquio syndrome who underwent aortic valve replacement surgery for severe aortic valve stenosis, with an uneventful postoperative course. Cardiac surgery appears safe and feasible in these patients and improves the quality of life, even if the future prognosis related to the underlying disorder should be considered.
More Related Videos
Related Concept Videos
Mitral Stenosis I: Introduction
Mitral Valve Prolapse I: Introduction
Mitral Stenosis III: Medical Management
Aortic Regurgitation III: Medical Management
Mitral Valve Prolapse II: Assessment and Management
Mitral Valve Prolapse III: Nursing Management

