Kimura disease of extremity: unusual manifestation in a long bone

Kimura's disease is a rare, chronic inflammatory disorder, presenting usually as head and neck swellings and regional cervical lymphadenopathy. The disease is more often described from oriental literature but the osseous manifestations and involvement of extremity are rare and unidentified in literature. We present an unusual case of long bone periosteal reaction in a patient of Kimura's disease of extremity. This potentially innocuous disorder must be kept in mind as a radiological differential of periosteal reaction.