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Updated: Jul 5, 2026
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Morphological and Functional Assessment of the Right Ventricle Using 3D Echocardiography
Published on: October 28, 2020
[Arrhythmogenic dysplasia of right ventricle: pathogenesis, genetic markers, clinical presentation, clinical example]
Klinicheskaia Meditsina
|May 23, 2008
Insights
Sudden cardiac death (SCD) is a complex condition often caused by coronary heart disease or cardiomyopathies. Arrhythmogenic right ventricle cardiomyopathy is one such heart muscle disease that can lead to SCD.
Area of Science:
- Cardiology and Cardiovascular Diseases
- Electrophysiology and Arrhythmias
- Genetic and Acquired Cardiomyopathies
Context:
- Sudden cardiac death (SCD) represents a significant clinical challenge, encompassing diverse cardiac pathologies.
- Coronary heart disease accounts for the majority of SCD cases, but cardiomyopathies are also a notable cause.
- Arrhythmogenic right ventricle cardiomyopathy (ARVC), also known as arrhythmogenic dysplasia of the right ventricle, is a specific form of cardiomyopathy.
Purpose:
- To elucidate the etiological spectrum of sudden cardiac death (SCD).
- To highlight the contribution of cardiomyopathies, including arrhythmogenic right ventricle cardiomyopathy (ARVC), to SCD.
- To provide a classification of cardiac pathologies leading to sudden cardiac death.
Summary:
- Sudden cardiac death (SCD) is an umbrella term for various heart conditions leading to abrupt fatality.
- While coronary heart disease is the leading cause (80%), cardiomyopathies, myocarditis, and congenital malformations contribute significantly (20%).
- Arrhythmogenic right ventricle cardiomyopathy (ARVC) is identified as a key type of cardiomyopathy implicated in SCD.
Impact:
- Improved understanding of SCD etiology can guide diagnostic and preventative strategies.
- Recognition of ARVC's role emphasizes the need for specialized screening in at-risk populations.
- This classification aids in research and clinical management of sudden cardiac death.
Abstract:
Sudden cardiac death (SCD) is a combined conception integrating various nosological forms of cardiac pathology. 80% of SCD cause is coronary heart disease, 20% are various cardiomyopathies, myocarditis, cardiovascular malformations and other rare diseases. One of cardiomyopathies is arrhythmogenic right ventricle cardiomyopathy or arrhythmogenic dysplasia of right ventricle.
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