Airway interventions in children with Pierre Robin Sequence

Abby C Meyer1, Michael E Lidsky, Daniel E Sampson

  • 1Children's Hospitals and Clinics of Minnesota-Minneapolis, Minneapolis, MN 55455, USA. stri0106@umn.edu

Insights

Over half of children with Pierre Robin Sequence (PRS) need airway interventions, including non-surgical and surgical options. Otolaryngologists must be prepared for managing these challenging pediatric airways.

Area of Science:

  • Pediatric Otolaryngology
  • Craniofacial Surgery
  • Airway Management

Background:

  • Pierre Robin Sequence (PRS) is a congenital condition characterized by micrognathia, glossoptosis, and airway obstruction.
  • Airway management in infants with PRS presents significant challenges due to their unique anatomy.

Purpose of the Study:

  • To detail the interventions necessary for effective airway management in pediatric patients diagnosed with Pierre Robin Sequence (PRS).

Main Methods:

  • A case series approach was employed, reviewing records from cleft/craniofacial and pediatric otolaryngology clinics.
  • Data extraction focused on feeding, airway interventions, and associated comorbidities in children with PRS.

Main Results:

  • Out of 74 identified PRS cases, 38 (over 50%) required airway intervention beyond prone positioning.
  • Non-surgical management (nasopharyngeal airway, endotracheal intubation) was used in 14 cases, while 24 required surgical intervention, including distraction osteogenesis and tracheostomy.

Conclusions:

  • A significant proportion of children with PRS necessitate airway interventions, encompassing both non-surgical and surgical methods.
  • Otolaryngologists must anticipate and be equipped to manage the complex airway challenges presented by children with PRS.
Abstract

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