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Pediatric otosclerosis: case report and literature review
Raquel Salomone1, Paulo Emmanuel Riskalla, Andy de Oliveira Vicente
1Hospital CEMA, Brazil.
Insights
Otospongiosis, a bone disorder affecting the temporal bone, can cause hearing loss in children. This case highlights an 11-year-old with unilateral hearing loss, emphasizing early diagnosis and management of otospongiosis in pediatric patients.
Area of Science:
- Otolaryngology
- Pediatric Otology
- Temporal Bone Pathology
Background:
- Otospongiosis is a temporal bone osteodystrophy causing progressive hearing loss and tinnitus.
- Typically, it affects adults in their third to fourth decade, presenting as conductive hearing loss.
- However, otosclerosis can uncommonly manifest in children and adolescents with conductive or sensorineural hearing loss.
Observation:
- A case study of an 11-year-old patient with a 5-year history of progressive unilateral conductive hearing loss.
- Clinical examination revealed a positive Schwartz's sign in the affected left ear.
- Audiometry, impedanciometry, and CT scans provided characteristic findings suggestive of otospongiosis.
Findings:
- The case demonstrates that otospongiosis can present in pediatric patients with progressive conductive hearing loss.
- Diagnostic tools like otoscopy, audiometry, impedanciometry, and CT scans are crucial for identifying otospongiosis in children.
- Schwartz's sign, though uncommon, can be an indicator of otospongiosis in pediatric cases.
Implications:
- This case underscores the importance of considering otospongiosis in the differential diagnosis of hearing loss in children and adolescents.
- Early identification and diagnosis are critical for timely intervention and management of otospongiosis in pediatric populations.
- Further research into the clinical aspects, diagnostic nuances, and therapeutic strategies for pediatric otospongiosis is warranted.
Abstract:
Otospongiosis is an osteodystrophy of the temporal bone, characterized by disordered neoformation and deposition of bone, characterized by the presence of a progressive conductive, sensorineural or mixed hearing loss and tinnitus. Typically, otospongiosis presents as a slowly progressive conductive hearing loss in the third to fourth decade of life. Uncommonly children and adolescents may also have conductive or sensorineural hearing loss caused by otosclerosis. We describe a case of an 11-year-old patient, with progressive unilateral conductive hearing loss for 5 years. The otoscopic examination revealed a positive Schwartz's sign in the left ear. Audiometry, impedanciometry and CT scan showed characteristics that suggested otospongiosis. We reviewed clinical aspects, diagnosis and the therapeutic approach for otospongiosis in children.

