Polysplenia syndrome in the asymptomatic adult: computed tomography evaluation

Although the majority of patients with polysplenia syndrome will present during infancy or childhood with congenital heart disease, 5% to 10% will have no cardiac disease; and the associated abnormalities may not be discovered until adulthood. Physicians should be familiar with the chest and abdominal radiographic findings so as not to confuse this syndrome with other, more common pathologic conditions in asymptomatic adult patients.