Pulmonary sequestration with right coronary artery supply

Area of Science:

• Cardiovascular Medicine
• Thoracic Surgery
• Pediatric Cardiology

Background:

• Pulmonary sequestration is a congenital lung malformation characterized by non-aerated lung tissue without communication to the normal tracheobronchial tree.
• Typically, these sequestrations receive systemic arterial supply from the thoracic aorta or its branches.
• Variations in vascular supply are documented but remain uncommon.

Observation:

• This report describes a rare case of intralobar pulmonary sequestration.
• The anomalous arterial supply to the sequestration originated directly from the right coronary artery.
• This vascular anomaly was identified in a patient presenting with respiratory symptoms.

Findings:

• The pulmonary sequestration demonstrated a unique systemic arterial supply originating from the right coronary artery.
• This finding deviates from the typical aortic or intercostal artery supply.
• Histopathological examination confirmed the nature of the sequestration and its vascular connection.

Implications:

• This case expands the known spectrum of vascular anomalies associated with pulmonary sequestration.
• Understanding such rare vascular origins is crucial for accurate diagnosis and surgical planning.
• Highlights the importance of comprehensive vascular imaging in managing complex congenital lung abnormalities.