Right ventricular myxoma obstructing the pulmonary artery during early childhood

Kiichiro Kumagai1, Sadahiro Sai, Masato Endo

  • 1Department of Cardiovascular Surgery, Graduate School of Medicine, Tohoku University, 1-1 Seiryo-machi, Aoba-ku, Sendai, Japan. kkumagai@mail.tains.tohoku.ac.jp

Insights

A rare right ventricular myxoma in a child caused pulmonary artery obstruction and cardiac arrest. Surgical removal was successful, with the patient recovering fully.

Area of Science:

  • Pediatric Cardiology
  • Cardiac Surgery
  • Pediatric Oncology

Background:

  • Primary cardiac tumors are rare in children.
  • Right ventricular myxomas are exceptionally uncommon in pediatric patients.
  • Early diagnosis and surgical intervention are crucial for managing pediatric cardiac tumors.

Observation:

  • A 2-year-old girl presented with a diagnosed right ventricular tumor.
  • The tumor caused obstruction of the pulmonary artery, leading to perioperative cardiac arrest.
  • The tumor was located in the right ventricular outflow tract.

Findings:

  • Successful surgical extirpation of the right ventricular myxoma was performed.
  • Cardiopulmonary bypass was initiated to manage the cardiac arrest and facilitate tumor removal.
  • The patient experienced an uncomplicated recovery and was discharged on postoperative day 13.

Implications:

  • This case highlights the importance of prompt diagnosis and surgical management of rare pediatric cardiac tumors.
  • Effective surgical techniques can lead to favorable outcomes even in complex cases with perioperative complications.
  • Further research into the etiology and optimal treatment strategies for pediatric cardiac myxomas is warranted.

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