[Spontaneous temporal bone meningo-encephalocele]

Paweł K Burduk1, Józef Mierzwiński, Danuta Burduk

  • 1Katedra i Klinika Otolaryngologii CM w Bydgoszczy UMK w Toruniu. pburduk@wp.pl

Abstract

Insights

Spontaneous meningoencephalocele of the temporal bone is rare, often linked to obesity and misdiagnosed. Surgical repair can resolve symptoms like pulsatile tinnitus, though hearing loss may persist.

Area of Science:

  • Neurology
  • Otolaryngology
  • Neurosurgery

Background:

  • Spontaneous meningoencephalocele of the temporal bone is exceptionally rare, often resulting from otologic surgery or head trauma.
  • Pathologic obesity is a potential contributing factor, with lesions typically occurring in the epitympanum or mastoid antrum.
  • These conditions are frequently misdiagnosed due to subtle or absent symptoms.

Observation:

  • A case study of a 61-year-old obese woman with spontaneous meningoencephalocele of the left temporal bone is presented.
  • The patient exhibited symptoms including conductive hearing loss, left ear fullness, and pulsatile tinnitus.
  • Imaging studies (CT and MRI) revealed tegmen dehiscent areas and meningoencephalocele protruding into the left mastoid cavity.

Findings:

  • Surgical intervention involved a left temporal bone mastoidectomy to address the meningoencephalocele.
  • The bony defect and cerebrospinal fluid (CSF) leak were successfully repaired during surgery.
  • Post-operatively, the patient experienced resolution of pulsatile tinnitus and ear fullness, with residual hearing dysfunction.

Implications:

  • Spontaneous meningoencephalocele in obese patients presents with characteristic symptoms like middle ear effusion and conductive hearing loss.
  • Combined CT and MRI imaging are crucial for accurate preoperative diagnosis.
  • Surgical approaches, including transmastoid or middle cranial fossa repair with multilayered defect closure, are essential to prevent CSF leaks.

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