Left-sided cervical aortic arch associated with pseudocoarctation, aneurysm formation, and anomalous left

Nabil J Khoury1, Roula Hourani, Ghina A Birjawi

  • 1Department of Diagnostic Radiology, American University of Beirut Medical Center, Beirut, Lebanon.

Insights

Cervical aortic arch (CAA), a rare congenital anomaly, can present with aneurysm and pseudocoarctation. This case report details an extremely rare combination of CAA with these conditions and a novel associated venous anomaly.

Area of Science:

  • Cardiovascular Medicine
  • Medical Imaging
  • Congenital Anomalies

Background:

  • Cervical aortic arch (CAA) is a rare congenital anomaly of the aorta.
  • CAA can be associated with various cardiovascular abnormalities, including aortic aneurysms and pseudocoarctation.
  • The combined occurrence of CAA with both aneurysm and pseudocoarctation is exceptionally rare.

Observation:

  • This report presents a unique case of cervical aortic arch (CAA).
  • The patient exhibited a rare combination of aortic aneurysm and pseudocoarctation.
  • An anomalous subaortic left brachiocephalic vein, not previously linked to CAA, was also identified.

Findings:

  • Multidetector computed tomography (MDCT) and magnetic resonance angiography (MRA) were used for imaging.
  • Radiographic findings confirmed the cervical aortic arch, aneurysm, and pseudocoarctation.
  • The anomalous venous structure was visualized and documented.

Implications:

  • This case expands the spectrum of known cardiovascular abnormalities associated with CAA.
  • The findings highlight the importance of comprehensive imaging in diagnosing complex congenital aortic anomalies.
  • The description of a novel venous anomaly associated with CAA may prompt further research into embryological development and clinical correlations.

Related Concept Videos

Aneurysm II: Clinical Manifestations and Diagnostic Studies01:21

Aneurysm II: Clinical Manifestations and Diagnostic Studies

Thoracic, aortic arch and abdominal aneurysms are significant vascular conditions that can present with various clinical manifestations and lead to serious complications. Understanding these manifestations and the appropriate diagnostic studies is essential for effective management and treatment.Thoracic Aortic AneurysmsThoracic aortic aneurysms often remain asymptomatic until they reach a size that impinges on adjacent structures. They typically cause deep, diffuse chest pain that radiates to...
The Arch of Aorta01:10

The Arch of Aorta

The coronary arteries, originating from the ascending aorta, bifurcate from two sinuses located within the ascending aorta. Positioned just above the aortic semilunar valve, these sinuses house essential aortic baroreceptors and chemoreceptors, crucial for maintaining cardiac function. The left coronary artery and the right coronary artery branch off from the left posterior and anterior aortic sinuses, respectively.
Encircling the heart, the coronary arteries form a ring-like structure before...
Aneurysm I: Introduction01:30

Aneurysm I: Introduction

An aortic aneurysm is a localized outpouching or dilation at a weak point in the artery wall. It may involve different parts of the aorta, such as the abdominal aorta, aortic arch, or thoracic aorta.Etiological factorsSeveral disorders are associated with aortic aneurysms.Congenital causes, such as primary connective tissue disorders like Marfan syndrome, impact the integrity and strength of connective tissues, notably affecting the aorta. Marfan syndrome is a genetic disorder that specifically...
Aortic Regurgitation II: Clinical Features and Diagnostic Tests01:22

Aortic Regurgitation II: Clinical Features and Diagnostic Tests

Aortic valve regurgitation (AR) occurs when the aortic valve fails to close properly, allowing blood to flow backward from the aorta into the left ventricle. This backflow can result in two distinct clinical presentations: acute and chronic AR, each characterized by its own set of symptoms and physical findings.Acute Aortic RegurgitationAcute AR presents with a sudden onset of severe symptoms. Patients typically experience profound dyspnea (shortness of breath), chest pain, and signs of left...
Thoracic Aorta01:15

Thoracic Aorta

The thoracic section of the aorta begins at the T5 vertebra and extends to the T12 level at the diaphragm, initially progressing through the mediastinum to the left of the spinal column. Throughout its course in the thoracic segment, the thoracic aorta emits various offshoots known collectively as visceral and parietal branches. The branches that predominantly supply blood to visceral organs are termed visceral branches and include bronchial, pericardial, esophageal, and mediastinal arteries,...
Veins of Thorax01:19

Veins of Thorax

The azygos system is a crucial part of the body's circulatory system and drains most of the thorax. It comprises the azygos, hemiazygos, and accessory hemiazygos veins.
The azygos vein, positioned just right of the midline and anterior to the vertebral column, begins at the junction of the right ascending lumbar and subcostal veins, terminating in the superior vena cava. This vein drains blood from the right side of the thoracic wall, thoracic viscera, and posterior abdominal wall.
The...