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Morphological and Functional Assessment of the Right Ventricle Using 3D Echocardiography
Published on: October 28, 2020
Double-outlet left ventricle: diagnosis and management
Shaji C Menon1, Donald J Hagler
1Mayo Clinic College of Medicine, 200 First Street SW, Rochester, MN 55905, USA.
Double-outlet left ventricle (DOLV) is a rare congenital heart defect where both great arteries arise from the left ventricle. Surgical repair often involves VSD closure and conduit placement, with alternatives like pulmonary root translocation.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Double-outlet left ventricle (DOLV) is a rare congenital cardiac malformation.
- It is characterized by both great arteries originating predominantly from the morphologic left ventricle.
- DOLV most commonly presents with atrial situs solitus and atrioventricular concordance, often with subaortic ventricular septal defects (VSD) and pulmonary stenosis.
Purpose of the Study:
- To describe the characteristics and common presentations of Double-outlet left ventricle (DOLV).
- To outline the conventional surgical treatments for DOLV with two well-developed ventricles.
- To mention alternative surgical approaches and management for specific DOLV patient subgroups.
Main Methods:
- Review of existing literature and case studies on Double-outlet left ventricle (DOLV).
- Analysis of common anatomical variations, associated defects, and clinical presentations.
- Description of established and alternative surgical repair strategies.
Main Results:
- DOLV typically involves pulmonary outflow obstruction, leading to cyanosis in newborns.
- Conventional surgical repair for DOLV with two ventricles includes VSD closure and right ventricle-to-pulmonary artery conduit.
- Pulmonary root translocation and Fontan procedures are alternative or necessary interventions for specific DOLV presentations.
Conclusions:
- Double-outlet left ventricle (DOLV) requires complex surgical management tailored to the specific anatomy.
- Early diagnosis and appropriate surgical intervention are crucial for improving outcomes in patients with DOLV.
- Treatment strategies range from biventricular repair to single-ventricle palliation depending on ventricular function and associated defects.
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