Treatment of persistent hyperplastic primary vitreous

Persistent hyperplastic primary vitreous (PHPV) will usually lead to a cataract and secondary glaucoma if not treated. At least a lensectomy should be performed to reduce the frequent incidence of glaucoma. In the purely anterior form, the cataract should be removed as well as the PHPV, as this gives a clear media that can be rehabilitated visually. Eyes with a posterior PHPV have poor visual results due to posterior pole abnormalities.