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Sick sinus syndrome and primary systemic amyloidosis
K Ramcharan1, C Harnarayan, H McFarlane
1San Fernando General Hospital, Trinidad.
The West Indian Medical Journal
|June 1, 1991
Summary
Sick sinus syndrome may indicate an underlying IgA Kappa paraproteinemia, a type of amyloidosis. Early exclusion of plasma cell dyscrasias is crucial for unexplained sick sinus syndrome cases.
Area of Science:
- Cardiology
- Hematology
- Oncology
Background:
- Sick sinus syndrome (SSS) is a common cardiac arrhythmia often requiring pacemaker implantation.
- Systemic amyloidosis is a progressive condition caused by abnormal protein deposits in organs.
Observation:
- A 68-year-old woman initially diagnosed with SSS later developed systemic amyloidosis.
- The amyloidosis diagnosis revealed an underlying IgA Kappa paraproteinemia.
Findings:
- This case highlights a rare association between SSS and IgA Kappa paraproteinemia-related systemic amyloidosis.
- Literature review indicates a potential link between plasma cell dyscrasias and SSS.
Implications:
- Unexplained sick sinus syndrome warrants investigation for underlying plasma cell dyscrasias.
- Early diagnosis of paraproteinemia can guide management and potentially alter prognosis in SSS patients.