Microscopic polyangiitis: a rare ANCA-associated small-vessel vasculitis

Microscopic Polyangiitis (MPA) is an autoimmune disease characterized by pauci-immune, necrotizing, small-vessel vasculitis without clinical or pathological evidence of necrotizing granulomatous inflammation. Because many different organ systems may be involved, a wide range of symptoms are possible in MPA. Cutaneous involvement is not frequent. We describe a young girl who presented with multiple vasculitic skin lesions along with arthralgia and after the onset of illness it took 4 years for appropriate diagnosis and management of the disease.