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Updated: Aug 15, 2026
09:22
Chronic Thromboembolic Pulmonary Hypertension and Assessment of Right Ventricular Function in the Piglet
Published on: November 4, 2015
Intralobar pulmonary sequestration
1Department of Surgery, Royal Children's Hospital Melbourne, Parkville, Victoria, Australia.
Progress in Pediatric Surgery
|January 1, 1991
Summary
Intralobar pulmonary sequestration is a rare congenital lung anomaly. Early diagnosis is crucial for managing associated cardiac issues or persistent respiratory infections in children.
Area of Science:
- Pediatric Surgery
- Congenital Anomalies
- Pulmonology
Background:
- Intralobar pulmonary sequestration (IPS) is a rare congenital anomaly.
- It involves non-functioning lung tissue lacking normal bronchial and vascular connections.
- IPS presents distinct clinical challenges in infants and older children.
Purpose of the Study:
- To describe the clinical presentations of intralobar pulmonary sequestration.
- To highlight the diagnostic considerations for this rare congenital anomaly.
- To emphasize the importance of timely management.
Main Methods:
- Review of clinical presentations of intralobar pulmonary sequestration.
- Analysis of diagnostic pathways for congenital lung anomalies.
- Discussion of definitive management strategies.
Main Results:
- Infants may present with significant arterio-venous shunts and cardiac anomalies.
- Older children often exhibit persistent radiological changes and treatment resistance post-infection.
- Definitive management involves shunt occlusion or sequestration removal.
Conclusions:
- Intralobar pulmonary sequestration requires consideration in specific pediatric clinical scenarios.
- Early recognition and appropriate cardiovascular investigations are vital for infants.
- Persistent respiratory symptoms unresponsive to treatment warrant further evaluation for IPS in older children.
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