[Orbital neurofibrosarcoma. Clinical and etiological study; apropos of a case]

This case report is about a relapsing conjunctive sarcoma affecting a 67 year old woman, involved with Von Recklinghausen's neurofibromatosis. Surgical orbital exenteration was necessary for curative treatment and reconstruction used a temporal muscle flap. Through this report, emphasis is placed on diagnosis difficulties and possibility of serious development concerning these malignant tumors in the scope of neurofibromatosis.