Small papillary tumor in the saccule

Papillary tumors of the ear are aggressive neoplasms. Previously, a tumor growing in the saccule had not been reported. We report a tumor found incidentally in the saccule of a patient. Serial sections of both temporal bones of the patient were studied in order to analyze the tumor's origin and influence on audio vestibular function. In the right inner ear, there was a small papillary lesion in the saccule, which looked like a papillary tumor without aggression invasion. The tumor was located in the membranous labyrinth of the saccule, not in the endolymphatic duct and sac. It was not related to Von Hippel-Lindau (VHL) disease, nor was it an endolymphatic sac tumor. The tumor did not influence the hearing and vestibular function in the right ear, although this patient presented a severe sensorineural hearing loss and vestibular function loss because of the vestibular schwannoma in the left ear.