Pupillary block glaucoma in child with persistent hyperplastic primary vitreus--case report

Krystyna Kanigowska1, Mirosława Grałek, Wiesława Grajkowska

  • 1Department of Ophthalmology of Children's Memorial Health Institute, Warsaw.

Klinika Oczna
|December 31, 2008
PubMed

Insights

Persistent hyperplastic primary vitreous (PHPV) can lead to pupillary block glaucoma due to lens dislocation. Early surgical intervention is crucial for managing this condition and preserving vision in affected infants.

Area of Science:

  • Ophthalmology
  • Pediatric Ophthalmology
  • Developmental Biology

Background:

  • Persistent hyperplastic primary vitreous (PHPV) is a congenital developmental disorder of the eye.
  • It can lead to various complications, including glaucoma and cataracts.

Observation:

  • A case of a 3-month-old infant with PHPV presenting with a grey pupillary reflex and microphthalmia.
  • The patient developed increased intraocular pressure and globe enlargement due to complete lens dislocation into the anterior chamber, causing pupillary block.

Findings:

  • A complex, one-step surgical procedure involving trabeculectomy, lensectomy, and removal of a retrolenticular fibrous membrane was performed.
  • The surgery successfully normalized intraocular pressure and facilitated visual rehabilitation. Transient choroidal detachment was noted postoperatively.

Implications:

  • This case highlights the critical role of early surgical intervention in managing PHPV complications like lens luxation and pupillary block.
  • Prompt treatment is essential to prevent irreversible pathological changes and optimize visual outcomes in affected children.
Abstract

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