Antenatally detected double prostatic utricle found in a neonate with ambiguous genitalia

Although enlarged prostatic utricle is usually seen in patients with hypospadias and disorders of sex development, double utricle has not been reported without unilateral renal dysplasia and Wolffian duct anomaly. We present an unusual case of antenatally detected large pelvic cyst, which turned out to be one of double prostatic utricles in a neonate with ambiguous genitalia. The possibility of enlarged utricle should be considered in the differential diagnosis of antenatally detected pelvic cysts in neonates with ambiguous genitalia.