[Tricuspid atresia associated with common trunk. A case report]

Area of Science:

• Pediatric Cardiology
• Congenital Heart Disease
• Cardiac Surgery

Background:

• Tricuspid atresia and persistent truncus arteriosus are rare congenital cardiac anomalies.
• Combined presentation requires complex management strategies.
• Early diagnosis and intervention are crucial for patient outcomes.

Observation:

• A 3-month-old male infant presented with a cardiac murmur.
• Echocardiography and cardiac catheterization confirmed the diagnosis.
• The infant had tricuspid atresia and persistent truncus arteriosus.

Findings:

• Surgical palliation involved pulmonary artery trunk disconnection and a 4 mm systemic-to-pulmonary shunt.
• The patient experienced persistent metabolic acidosis post-operatively.
• Mortality occurred within 24 hours of the initial surgical step.

Implications:

• This case highlights the challenges in managing complex congenital heart defects.
• Further research into optimal surgical approaches for this rare anomaly is warranted.
• Understanding the pathophysiology of post-operative metabolic acidosis is critical for improving survival rates.