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Behavioral Assessment of Hearing in 2 to 4 Year-old Children: A Two-interval, Observer-based Procedure Using Conditioned Play-based Responses
Published on: January 23, 2017
Ophthalmologic findings in children with sensorineural hearing loss
Arun Sharma1, Melissa N Ruscetta, David H Chi
1Department of Otolaryngology, University of Washington, Seattle, USA.
Archives of Otolaryngology--Head & Neck Surgery
|February 18, 2009
Summary
Approximately 21.7% of children with sensorineural hearing loss (SNHL) have ophthalmologic abnormalities. Routine eye exams are beneficial for these children, though anomalies are less common in those with GJB2 mutations.
Area of Science:
- Ophthalmology
- Genetics
- Pediatrics
Background:
- Sensorineural hearing loss (SNHL) can be associated with various medical conditions.
- Ophthalmologic abnormalities may coexist with SNHL, necessitating thorough evaluation.
Purpose of the Study:
- To determine the prevalence of refractive and nonrefractive ophthalmologic abnormalities in children diagnosed with SNHL.
- To assess the utility of routine ophthalmological examinations in pediatric patients with SNHL.
Main Methods:
- Retrospective analysis of ophthalmologic findings in children (≤18 years) with SNHL.
- Data collected from a tertiary care university children's hospital between 2000 and 2007.
Main Results:
- Of 226 children with SNHL, 49 (21.7%) exhibited ophthalmologic abnormalities.
- Refractive errors occurred in 10.2% and nonrefractive conditions in 12.8%.
- Ophthalmologic abnormalities were found in 3.7% of patients with GJB2 mutations versus 20.7% without (P=.04).
Conclusions:
- The overall prevalence of ophthalmologic findings in children with SNHL is 21.7%.
- Routine ophthalmologic examinations are valuable for evaluating children with SNHL.
- A lower prevalence of eye anomalies was noted in children with GJB2 mutations.
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