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Cholestasis caused by biliary botryoid sarcoma.
V N Perisic1, E R Howard, T Mihailovic
1Mother and Child Health Institute, Novi Beograd, Yugoslavia.
Summary
A rare botryoid sarcoma in a child caused bile duct obstruction. Surgical removal and chemotherapy were successful, with no signs of tumor recurrence.
Area of Science:
- Pediatric oncology
- Gastroenterology
- Surgical pathology
Background:
- Bile duct tumors are rare in children.
- Early diagnosis of pediatric choledochal tumors is crucial.
Observation:
- A 4-year-old boy presented with jaundice and hepatomegaly.
- Endoscopic retrograde cholangiopancreatography and percutaneous transhepatic cholangiography revealed a large obstructing choledochal tumor.
Findings:
- A botryoid sarcoma obstructing the common bile duct was surgically removed.
- Post-operative cytotoxic therapy led to persistent extrahepatic bile duct dilatation, requiring excision.
- No evidence of residual or recurrent tumor was found.
Implications:
- Botryoid sarcoma is a rare but treatable pediatric biliary tumor.
- Aggressive management including surgery and chemotherapy is effective.
- Potential complications like bile duct dilatation require monitoring and management.