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Published on: October 12, 2017
Retrocaval ureter: a rare cause of hydronephrosis in children
Samir Kant Acharya1, Bibekanand Jindal, Devendra Kumar Yadav
1Department of Pediatric Surgery, Safdarjung Hospital and Associated Vardhaman Mahavir Medical College, New Delhi 110029, India.
Insights
Retrocaval ureter, a rare congenital anomaly, can cause ureteric obstruction and flank pain. This case highlights a successful surgical correction in a pediatric patient, emphasizing early intervention for symptomatic cases.
Area of Science:
- Urology
- Pediatric Surgery
- Developmental Biology
Background:
- Retrocaval ureter is a rare congenital anomaly involving the inferior vena cava, typically presenting in adulthood.
- Pediatric cases are exceptionally uncommon, making diagnosis and management challenging.
- Symptomatic presentation is usually due to ureteric obstruction, necessitating surgical intervention.
Observation:
- A pediatric patient presented with flank pain and right hydronephrosis.
- Surgical evaluation revealed an undiagnosed retrocaval ureter anomaly.
- The anomaly involved the right ureter being obstructed by its passage behind the inferior vena cava.
Findings:
- Surgical correction involved dividing the ureter and re-anastomosing it anterior to the inferior vena cava.
- The procedure successfully relieved the ureteric obstruction and addressed the hydronephrosis.
- Histopathological examination confirmed the developmental nature of the anomaly.
Implications:
- This case underscores the importance of considering rare congenital anomalies in pediatric patients with unexplained urinary tract obstruction.
- Successful surgical management in childhood can prevent long-term renal damage and complications.
- Further research into the embryological origins of retrocaval ureter may improve diagnostic and therapeutic strategies.
Abstract:
Retrocaval ureter is a relatively rare developmental anomaly of the inferior vena cava. It commonly manifests in the third to fourth decade of life; however, pediatric reports of this condition are very rare. Individuals with this anomaly are symptomatic because of ureteric obstruction. All symptomatic patients need surgery where the ureter is divided and anastomosed anterior to inferior vena cava. We report our experience of a child who presented with flank pain and, on evaluation, were found to have right hydronephrosis. During surgery, retrocaval anomaly was noticed and appropriately dealt with.
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