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Cerebral venous thrombosis as the initial presentation of Behcet's disease

Ali Ibrahim Rahil1, Mehdi Errayes, Khaled M Salem

  • 1Department of medicine, Hamad General Hospital, Doha-Qatar. ali_eljazwi@yahoo.com

Chang Gung Medical Journal
|May 1, 2009
PubMed

Insights

Behcet

Area of Science:

  • Neurology
  • Rheumatology
  • Ophthalmology

Background:

  • Behcet's disease is a rare multisystem inflammatory disorder.
  • Neurological involvement, or neuro-Behcet's disease, is an uncommon but serious manifestation.
  • Cerebral venous thrombosis is a rare presentation of Behcet's disease.

Observation:

  • A 40-year-old man presented with headache, vision loss, and oral ulcers.
  • Clinical examination revealed oral ulcers, posterior synechia, and vision loss in the right eye.
  • Fundoscopy showed retinal vasculitis.

Findings:

  • Brain MRI and MRV confirmed superior sagittal, left transverse, and left sigmoid sinus venous thrombosis.
  • Diagnosis of Behcet's disease was established based on clinical criteria.
  • The patient experienced significant clinical improvement with immunosuppressive therapy and anticoagulation.

Implications:

  • This case highlights cerebral venous thrombosis as an initial presentation of Behcet's disease.
  • Early diagnosis and multidisciplinary management are crucial for favorable outcomes.
  • Understanding rare neurological manifestations aids in timely intervention for Behcet's disease.

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