Right atrial fibroma requiring emergent intervention in an 8-week-old infant
Matthew Oster1, Brian Kogon, Bahig Shehata
1Department of Cardiology, Sibley Heart Center, Emory University, Atlanta, GA, USA. matthew.oster@choa.org
Insights
This report details a rare right atrial fibroma in an 8-week-old infant, successfully treated with surgery. This case represents the youngest survivor of complete resection for this condition.
Area of Science:
- Pediatric Cardiology
- Pediatric Cardiac Surgery
- Pediatric Oncology
Background:
- Cardiac fibromas are rare pediatric tumors.
- Right atrial involvement is exceptionally uncommon.
- Infantile presentation often indicates aggressive disease.
Observation:
- An 8-week-old infant presented with acute profound shock.
- Echocardiography identified a large right atrial mass.
- The mass obstructed tricuspid valve blood flow.
Findings:
- Complete surgical resection of the right atrial fibroma was achieved.
- The infant is the youngest documented survivor of this procedure.
- Histopathological confirmation of fibroma was obtained.
Implications:
- Highlights the possibility of right atrial fibromas in neonates.
- Emphasizes the need for emergent intervention in symptomatic cases.
- Provides a benchmark for surgical outcomes in infant cardiac tumors.
Abstract:
Cardiac fibromas are extremely rare in children and typically do not involve the right atrium. We report the case of an 8-week-old infant with a right atrial fibroma who presented acutely in profound shock. Echocardiography revealed a large mass occupying the right atrium and obstructing flow through the tricuspid valve, prompting emergent surgical resection. To our knowledge, ours is the youngest patient to survive complete resection of a right atrial fibroma.
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