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Liver transplantation for syndromic biliary atresia with a pedunculated accessory hepatic lobe
Walid Faraj1, Faisal Dar, Gabriele Marangoni
1King's College London School of Medicine, Institute of Liver Studies, King's College Hospital, London, UK. wfaraj@hotmail.com
Insights
Extrahepatic biliary atresia (EHBA) is a common reason for pediatric liver transplants. This case highlights a left lobe transplant for syndromic EHBA, emphasizing the importance of considering complex congenital anomalies.
Area of Science:
- Pediatric Surgery
- Hepatology
- Transplantation Immunology
Background:
- Extrahepatic biliary atresia (EHBA) is the primary indication for liver transplantation in pediatric patients.
- Congenital malformations frequently accompany EHBA, occurring in 9%-37% of cases.
Observation:
- A pediatric patient with syndromic EHBA underwent a liver transplant.
- The transplant utilized a left lobe graft.
Findings:
- Successful left lobe liver transplantation was performed for a case of syndromic EHBA.
- This approach addresses the challenges posed by associated congenital anomalies in EHBA.
Implications:
- Left lobe liver transplantation is a viable option for infants and children with syndromic EHBA.
- Understanding associated malformations is crucial for optimizing surgical outcomes in pediatric liver transplantation.
Abstract:
Extrahepatic biliary atresia (EHBA) is the most common indication for liver transplantation in infants and children. Congenital malformations associated with EHBA are common and present in about 9%-37%. We describe a case of a child who received a left lobe liver transplant for syndromic EHBA.
