[Ebstein's anomaly and interventricular communication, a rare association]

Area of Science:

• Cardiology
• Congenital Heart Disease
• Pediatric Cardiology

Background:

• Ebstein's anomaly is a rare congenital heart defect characterized by malformation of the tricuspid valve.
• It typically involves displacement of the septal and posterior leaflets into the right ventricle.

Observation:

• This study reports three cases of Ebstein's anomaly associated with a ventricular septal defect (VSD), an uncommon combination.
• Patients presented with varying clinical manifestations, including acyanotic heart defect with congestive heart failure and cyanotic impairment.

Findings:

• Surgical interventions for Ebstein's anomaly and VSD showed diverse outcomes.
• One patient experienced a fatal outcome post-surgery, while two others showed functional improvement with different surgical approaches.
• Successful management depends on the VSD's characteristics and surgical technique.

Implications:

• The association of Ebstein's anomaly with VSD necessitates careful clinical judgment for accurate diagnosis and timely intervention.
• Understanding the impact of VSD size and location on pulmonary flow is crucial for surgical planning.
• This case series underscores the complexity and variability in managing this rare cardiac malformation.