[Primary pulmonary arterial hypertension and pregnancy. Case report]

Pregnancy is rarely associated with primary pulmonary hypertension (PPH). We are here presenting the case of a 28 year old patient who developed, during her second pregnancy, primary pulmonary hypertension, with fatal results. The autopsy confirmed the diagnosis. The analysis of the case and a review of the literature suggests that patients suffering from PPH are to be advised against pregnancy, or a therapeutic precocious interruption of the pregnancy is to be considered. In case of late discovery of PPH during pregnancy, peridural anesthetics while controlling the pulmonary blood pressure during the delivery seems to be the chosen technique.