Ameloblastomatous calcifying odontogenic cyst: a case report of a rare histologic variant

Calcifying odontogenic cyst is an uncommon developmental odontogenic cyst first described by Gorlin in 1962. It is considered as an extremely rare cyst and accounts for only 1% of jaw cysts reported. Because of its diverse histopathology, there has always been confusion about its nature as a cyst, neoplasm, or hamartoma. In this report, we present a rare case of calcifying odontogenic cyst with ameloblastic proliferation--an extremely rare histologic variant in a 22-year-old male in the right mandibular molar region. The lesion was surgically removed. After enucleation no recurrence has been recorded in the ensuing 14 months.