Endomyocardial fibrosis mimicking Ebstein's anomaly: a diagnostic challenge
Karthik Vaidyanathan1, Ravi Agarwal, Anto Sahayaraj
1Department of Cardiac Surgery, Frontier Lifeline, Dr. KM Cherian Heart Foundation, Chennai 600101, India. rkvdoc@rediffmail.com
Abstract:
Endomyocardial fibrosis is a rare disease that is seen most commonly in tropical countries. It usually presents with characteristics of right-heart failure. Herein, we report the case of a 14-year-old adolescent boy who experienced endomyocardial fibrosis. Upon transthoracic echocardiography, the condition was mistakenly diagnosed as Ebstein's anomaly of the tricuspid valve. Sixteen months after undergoing tricuspid annuloplasty and receiving a bidirectional Glenn shunt, the patient showed no echocardiographic evidence of valvular regurgitation. We discuss imaging and surgical techniques that enable the diagnosis and treatment of endomyocardial fibrosis.
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