Dyschromatosis universalis hereditaria in a young Nigerian female

S M Yusuf1, M S Mijinyawa, M B Maiyaki

  • 1Department of Medicine, Aminu Kano Teaching Hospital, Nigeria. shehumy@yahoo.com

Dyschromatosis universalis hereditaria (DUH) is a clinically heterogeneous disorder that shows generalized mottled pigmentation. It occurs most commonly in Japanese persons, with sporadic reports from South Africa, India, and Iraq. Histopathology reveals a variable degree of pigmentary incontinence. Although the precise etiology of this disorder is not yet known, the clinicopathological findings implicate an inherent abnormality of melanosomes or melanin processing. We describe a case in a young Nigerian girl.

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