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Updated: Jun 21, 2026

Increasing Pulmonary Artery Pulsatile Flow Improves Hypoxic Pulmonary Hypertension in Piglets
Published on: May 11, 2015
Pediatric pulmonary arterial hypertension--a review
Sunita Juliana Ferns1, William H Wehrmacher, Maria Serratto
1Department of Pediatrics, University of Illinois at Chicago, 840 St, Wood St, Chicago IL 60612, USA. sjulianaferns@yahoo.com
Abstract:
Pulmonary arterial hypertension (PAH) afflicts thousands of children worldwide. The pathophysiology involves intravascular proliferation and remodeling leading to an increase in pulmonary vascular resistance which if left untreated results in right heart failure and death. Signs and symptoms are subtle as the disease progresses to irreversible lung damage. There is no cure for PAH, however newer methods of treatment can successfully manage these patients and delay progression of the disease process.
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