Related Experiment Video

Updated: Jan 14, 2026

Implementation of Non-invasive Point of Care Transient Elastography for Evaluation of Liver Disease in Pediatric Populations with Cystic Fibrosis
05:56

Implementation of Non-invasive Point of Care Transient Elastography for Evaluation of Liver Disease in Pediatric Populations with Cystic Fibrosis

Published on: August 29, 2025

429

[Hepatopulmonary syndrome in children: evaluation and treatment]

S Rovira Amigo1, C Martín de Vicente, J Bueno Recio

  • 1Unidad de Neumología Pediátrica y Fibrosis Quística, Hospital Universitari Vall d'Hebron, Barcelona, España. 42402sra@comb.cat

Anales De Pediatria (Barcelona, Spain : 2003)
|July 31, 2009
PubMed

Insights

Hepatopulmonary syndrome, a rare liver disease complication, presents with hypoxemia and intrapulmonary shunting. This study details five pediatric cases, highlighting varied disease types and tailored therapeutic strategies for improved outcomes.

Area of Science:

  • Medicine
  • Cardiology
  • Pulmonology

Background:

  • Hepatopulmonary syndrome (HPS) is a rare complication of liver disease, affecting patients of all ages.
  • Diagnosis relies on identifying hypoxemia and intrapulmonary shunting via imaging techniques.

Observation:

  • This study presents five pediatric cases of hepatopulmonary syndrome.
  • The cases exhibited diverse natural histories and clinical evolutions.

Findings:

  • Two patients were diagnosed with HPS type 1, and two with HPS type 2.
  • One patient presented with features of both HPS type 1 and type 2.

Implications:

  • The distinct HPS types necessitate individualized therapeutic approaches.
  • Understanding these classifications is crucial for effective pediatric HPS management.

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